The nurse is educating a parent after the birth of a newborn who is diagnosed with phenylketonuria (PKU). Which parent statement indicates teaching has been effective?
"The concern is the baby has an excess of a liver enzyme."
"My infant will be on a low iron formula."
"My infant will be on a low protein formula."
"Once the baby is on solid foods, the dietary restriction will be gone."
The Correct Answer is C
Choice A reason: PKU is caused by a deficiency of the liver enzyme phenylalanine hydroxylase, not an excess. This enzyme is needed to convert phenylalanine into tyrosine. Without it, phenylalanine accumulates and causes neurotoxicity. This statement reflects a misunderstanding of the condition.
Choice B reason: Iron levels are not the focus of dietary management in PKU. While iron is important for growth and development, the primary concern is controlling phenylalanine intake through protein restriction. Low iron formula is not indicated unless there is a separate iron-related issue.
Choice C reason: A low protein formula is essential for infants with PKU because phenylalanine is found in high-protein foods. Specialized formulas are designed to provide adequate nutrition while limiting phenylalanine intake. This statement demonstrates accurate understanding of dietary management.
Choice D reason: Dietary restrictions for PKU are lifelong. Solid foods must also be carefully selected to avoid high phenylalanine content. The idea that restrictions end with solid food introduction is incorrect and potentially harmful.
Nursing Test Bank
Naxlex Comprehensive Predictor Exams
Related Questions
Correct Answer is ["A","B","E"]
Explanation
Choice A rationale
Placing the neonate, who is anticipated to be vigorous based on the current reassuring fetal status (baseline 145, moderate variability, accelerations), directly onto the mother's chest, skin-to-skin, facilitates thermoregulation through maternal heat transfer. This action also promotes bonding and encourages early breastfeeding, releasing oxytocin for uterine involution. Immediate drying prevents evaporative heat loss, and the mother's chest provides a warm, stable thermal environment, crucial for stabilizing the newborn's core temperature and vital signs.
Choice B rationale
Routine drying and warming are essential immediate steps for all newborns to prevent hypothermia, which increases metabolic demands and oxygen consumption. Evaporative heat loss from amniotic fluid is significant; drying removes this fluid. Warming measures, such as pre-warmed blankets or radiant warmer, are critical to maintain the newborn's thermoregulation and achieve a target temperature of 36.5°C to 37.5°C (97.7°F to 99.5°F), preventing cold stress which can lead to hypoglycemia and metabolic acidosis.
Choice C rationale
Hyperbilirubinemia, or neonatal jaundice, typically manifests as a serum total bilirubin level above 5 mg/dL and is generally a later post-delivery finding, often peaking between 3 to 5 days of life, not an immediate one. While factors like prematurity (38 weeks is term, ≥ 37 weeks), prolonged rupture of membranes (19 hours), and potential infection (chorioamnionitis risk) can slightly increase risk, it is not an anticipated immediate concern at delivery, and thus requires close postnatal monitoring, not immediate delivery preparation.
Choice D rationale
Immediate transfer to the Neonatal Intensive Care Unit (NICU) is reserved for newborns with severe distress, significant congenital anomalies, or requiring complex support, such as immediate endotracheal intubation. Given the current reassuring fetal heart rate (FHR) tracing (moderate variability, accelerations, early decelerations), a severely compromised infant requiring immediate intensive care is not anticipated. The FHR's recovery from the prior deceleration suggests the fetus has currently compensated well, supporting a plan for routine or slightly enhanced delivery care.
Choice E rationale
Although the current FHR is reassuring, the history of prolonged rupture of membranes (19 hours), Pitocin augmentation, and a prior episode of uterine tachysystole with a 4-minute prolonged deceleration elevates the risk for perinatal asphyxia or meconium aspiration (though fluid was clear). Therefore, having suction (bulb syringe, deep suction equipment) and oxygen delivery systems (free-flow oxygen, Positive Pressure Ventilation (PPV) device) immediately ready is a standard and prudent precautionary measure for any potential unexpected neonatal resuscitation need.
Choice F rationale
Respiratory depression is commonly associated with maternal opioid administration close to delivery or severe perinatal asphyxia. Despite the earlier FHR changes, the current tracing is reassuring, and the mother did not receive recent depressant medications, thus significant respiratory depression is improbable. While all newborns have a risk of transient tachypnea, severe, immediate respiratory depression necessitating immediate ventilation is not the primary expected outcome given the current fetal status.
Choice G rationale
Positive Pressure Ventilation (PPV) is indicated if the newborn is apneic, gasping, or has a heart rate below 100 beats per minute despite drying and stimulation. The current reassuring FHR tracing makes an immediate need for PPV unlikely. Preparation for PPV is required as per Choice E, but the immediate need is not anticipated, as the fetus currently appears stable and non-acidotic, suggesting a transition requiring only minimal support.
Choice H rationale
A Stat Cesarean Section is indicated for non-remediable, persistent Category III FHR tracings, such as absent variability with recurrent late/variable decelerations or a sinusoidal pattern, which indicate severe fetal compromise. The current FHR tracing is Category I (reassuring), with a normal baseline and moderate variability. Therefore, a Stat Cesarean Section is contraindicated and unnecessary; the delivery should proceed vaginally as planned. —. ##
Correct Answer is C
Explanation
Choice A reason: Fluid restriction is contraindicated in cystic fibrosis. These children are prone to dehydration due to excessive salt loss in sweat. Adequate hydration is essential, especially during infections.
Choice B reason: Physical activity is encouraged in children with cystic fibrosis as it helps improve lung function, mobilize secretions, and enhance overall well-being. Restriction is not recommended unless medically indicated.
Choice C reason: Pancreatic enzyme replacement is critical in cystic fibrosis due to pancreatic insufficiency. Enzymes must be taken with all meals and snacks to aid digestion and nutrient absorption. This is a cornerstone of nutritional management.
Choice D reason: Children with cystic fibrosis require high-calorie, high-protein diets to meet increased metabolic demands and support growth. A low-calorie, low-protein diet would be inappropriate and harmful.
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