A 9-month-old with Tay-Sachs disease is admitted due to seizures. Which assessment is most important for the nurse to obtain?
Ability to crawl.
Eyes with cherry-red spot.
Difficulty with swallowing.
Exaggerated startle reaction
The Correct Answer is D
Choice A reason: The ability to crawl is not the most important assessment for the nurse to obtain. Tay-Sachs disease causes progressive loss of motor skills, so the infant may not be able to crawl or may have regressed from crawling. However, this is not a specific sign of the disease and does not indicate the severity of the condition.
Choice B reason: The eyes with cherry-red spot are not the most important assessment for the nurse to obtain. Tay-Sachs disease causes accumulation of gangliosides in the retina, which results in a cherry-red spot in the center of the macula. However, this is not a specific sign of the disease and does not indicate the severity of the condition.
Choice C reason: The difficulty with swallowing is not the most important assessment for the nurse to obtain. Tay-Sachs disease causes muscle weakness and spasticity, which may affect the infant's ability to swallow. However, this is not a specific sign of the disease and does not indicate the severity of the condition.
Choice D reason: The exaggerated startle reaction is the most important assessment for the nurse to obtain. Tay-Sachs disease causes increased sensitivity to sound and touch, which results in an exaggerated startle reaction. This is a specific sign of the disease and indicates the severity of the condition. The exaggerated startle reaction may also trigger seizures, which can be life-threatening. The nurse should monitor the infant's vital signs, seizure activity, and neurological status closely.
Nursing Test Bank
Naxlex Comprehensive Predictor Exams
Related Questions
Correct Answer is A
Explanation
Choice A reason: Instilling benzocaine otic drops regularly is not a recommended practice for preventing or treating otitis media. Benzocaine is a topical anesthetic that can temporarily relieve ear pain, but it does not address the underlying cause of the infection. Moreover, benzocaine can cause allergic reactions, skin irritation, or methemoglobinemia, a condition that reduces the oxygen-carrying capacity of the blood. The nurse should instruct the caregiver to avoid using benzocaine otic drops unless prescribed by a health care provider.
Choice B reason: Avoiding any smoking inside the house is a good practice for preventing otitis media. Smoking can irritate the respiratory tract and impair the function of the cilia, the hair-like structures that help clear mucus and bacteria from the middle ear. Smoking can also increase the risk of respiratory infections, allergies, and asthma, which are associated with otitis media. The nurse should praise the caregiver for avoiding smoking and encourage them to maintain a smoke-free environment for the infant.
Choice C reason: Giving the infant the full course of antibiotics is a necessary practice for treating otitis media. Antibiotics can help eliminate the bacteria that cause the infection and reduce the inflammation and pain in the middle ear. However, antibiotics should be used only when prescribed by a health care provider, and the caregiver should follow the instructions carefully. The nurse should remind the caregiver to give the infant the exact dose of antibiotics at the right time and for the entire duration of the treatment, even if the symptoms improve.
Choice D reason: Scheduling a visit for pneumococcal vaccine is a preventive measure for otitis media. Pneumococcal vaccine can protect the infant from the most common strains of Streptococcus pneumoniae, a bacterium that causes otitis media and other serious infections. The vaccine is recommended for all children under 2 years of age, and it is given in four doses at 2, 4, 6, and 12 to 15 months of age. The nurse should verify the infant's immunization status and advise the caregiver to follow the recommended schedule for the pneumococcal vaccine.
Correct Answer is B
Explanation
Choice A reason: Rhabdomyolysis is not the probable cause of the findings. Rhabdomyolysis is a condition that occurs when damaged muscle tissue breaks down and releases substances into the bloodstream that can harm the kidneys. It is usually caused by trauma, infection, drugs, or extreme exercise. It does not cause radial ossification in the soft tissues, but rather dark urine, muscle weakness, and kidney failure.
Choice B reason: Osteosarcoma is the probable cause of the findings. Osteosarcoma is a type of bone cancer that usually affects the long bones of the arms and legs. It is more common in adolescents and young adults. It can cause pain, swelling, and limping in the affected area, as well as radial ossification in the soft tissues, which is a sign of tumor invasion.
Choice C reason: Growing pains are not the probable cause of the findings. Growing pains are a common cause of leg pain in children and adolescents, but they are not associated with any physical abnormality or disease. They usually occur in both legs, not just one, and they are more likely to affect the calves, shins, or thighs, not the knees. They do not cause swelling, tenderness, or radial ossification in the soft tissues.
Choice D reason: Hemosiderosis is not the probable cause of the findings. Hemosiderosis is a condition that occurs when excess iron deposits in the tissues, usually as a result of repeated blood transfusions or hemolytic anemia. It can affect various organs, such as the liver, lungs, heart, and skin, but not the bones. It does not cause pain, swelling, or radial ossification in the soft tissues, but rather fatigue, shortness of breath, chest pain, and skin discoloration.
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