A client with cystic fibrosis (CF) is concerned about how this condition affects their body.
The client asks, "Why does CF lead to the production of thick mucus in the lungs and other organs?" Which of the following responses by the nurse is accurate?
"The CFTR gene mutation causes excessive water transport in the body.”
"CF results in an overproduction of a specific enzyme that thickens mucus.”
"The CFTR gene mutation impairs chloride and water transport in cells.”
"CF primarily affects the production of surfactant in the lungs.”
The Correct Answer is C
"The CFTR gene mutation impairs chloride and water transport in cells.”.
Choice A rationale:
The CFTR gene mutation does not cause excessive water transport in the body.
In fact, CF leads to a defect in chloride and water transport in cells, which results in the production of thick mucus.
Choice B rationale:
CF does not result in an overproduction of a specific enzyme that thickens mucus.
Instead, it affects the functioning of the CFTR protein, which is responsible for maintaining the balance of chloride and water in cells.
Choice D rationale:
CF does not primarily affect the production of surfactant in the lungs.
Surfactant is a substance that helps prevent the collapse of alveoli in the lungs, and CF primarily affects the mucus and airway clearance, not surfactant production.
Nursing Test Bank
Naxlex Comprehensive Predictor Exams
Related Questions
Correct Answer is ["A","B","D","E"]
Explanation
Choice A rationale:
Encouraging physical activity and exercise is important in managing CF.
It helps improve lung function and overall health in individuals with CF.
Choice B rationale:
Administering pancreatic enzyme replacement therapy is a crucial part of CF management.
CF often affects the pancreas, leading to malabsorption, and these enzymes help digest and absorb nutrients properly.
Choice C rationale:
Restricting fluid intake to reduce mucus production is not a recommended intervention for CF.
Hydration is essential to keep mucus from becoming too thick and sticky.
Dehydration can worsen mucus obstruction.
Choice D rationale:
Teaching airway clearance techniques is essential in CF management.
It helps individuals clear the thick mucus from their airways, promoting better lung function.
Choice E rationale:
Promoting a high-fat, high-calorie diet is important for individuals with CF.
CF often leads to malnutrition, and a high-calorie diet helps maintain proper nutrition and growth.
Correct Answer is B
Explanation
"CF is an autosomal recessive genetic disorder.”.
Choice A rationale:
CF is not inherited through an X-linked dominant pattern.
X-linked inheritance involves genes located on the X chromosome, and CF is not linked to this type of inheritance.
Choice C rationale:
CF is not solely related to inheriting a defective CFTR gene from one parent.
While inheriting a mutated CFTR gene is a factor, CF is an autosomal recessive disorder, meaning it requires mutations in both copies of the CFTR gene (one from each parent) for the disease to manifest.
Choice D rationale:
CF is not solely caused by the deletion of phenylalanine at position 508 (F508del).
While this mutation is one of the most common causes of CF, it is not the only genetic variation associated with the disease.
CF can result from various mutations in the CFTR gene.
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