A nurse is teaching a group of parents about managing cystic fibrosis (CF) in children.
Which of the following interventions should the nurse include in the teaching? (Select all that apply).

Choice A rationale:

Encouraging physical activity and exercise is important in managing CF.

It helps improve lung function and overall health in individuals with CF.

Choice B rationale:

Administering pancreatic enzyme replacement therapy is a crucial part of CF management.

CF often affects the pancreas, leading to malabsorption, and these enzymes help digest and absorb nutrients properly.

Choice C rationale:

Restricting fluid intake to reduce mucus production is not a recommended intervention for CF.

Hydration is essential to keep mucus from becoming too thick and sticky.

Dehydration can worsen mucus obstruction.

Choice D rationale:

Teaching airway clearance techniques is essential in CF management.

It helps individuals clear the thick mucus from their airways, promoting better lung function.

Choice E rationale:

Promoting a high-fat, high-calorie diet is important for individuals with CF.

CF often leads to malnutrition, and a high-calorie diet helps maintain proper nutrition and growth.

"The CFTR gene mutation impairs chloride and water transport in cells.”.

Choice A rationale:

The CFTR gene mutation does not cause excessive water transport in the body.

In fact, CF leads to a defect in chloride and water transport in cells, which results in the production of thick mucus.

Choice B rationale:

CF does not result in an overproduction of a specific enzyme that thickens mucus.

Instead, it affects the functioning of the CFTR protein, which is responsible for maintaining the balance of chloride and water in cells.

Choice D rationale:

CF does not primarily affect the production of surfactant in the lungs.

Surfactant is a substance that helps prevent the collapse of alveoli in the lungs, and CF primarily affects the mucus and airway clearance, not surfactant production.