The nurse is caring for a child with a diagnosis of Kawasaki disease. The child's parent asks the nurse, "How does Kawasaki disease affect my child's heart and blood vessels?" On what understanding is the nurse's response based?

A. Wheezing. Cystic fibrosis can cause airway obstruction due to thickened mucus, leading to wheezing and difficulty breathing, especially during respiratory infections or exacerbations.

B. A barrel-shaped chest is often seen in advanced stages of cystic fibrosis. It results from hyperinflation of the lungs due to air trapping, chronic lung disease, and repeated respiratory infections. The chest appears rounded and enlarged, similar to the shape of a barrel.

D. Clubbing of fingers and toes is a common finding in cystic fibrosis. It is caused by chronic hypoxia and inadequate oxygenation of tissues, leading to changes in the nail beds and fingertips. Clubbing typically develops over time in individuals with chronic respiratory conditions, including cystic fibrosis.

C. Thin, watery mucous is not expected in cystic fibrosis. Instead, cystic fibrosis is characterized by thick, sticky mucus due to dysfunction of the exocrine glands, leading to blockages in the airways, pancreas, and other organs.

E. Rapid growth spurts are not typically associated with cystic fibrosis. In fact, children with cystic fibrosis may experience growth failure or delayed growth due to malabsorption of nutrients, chronic illness, and increased energy expenditure.

D. Pancreatic enzymes should not be mixed with acidic foods or liquids, as this can reduce their effectiveness. Instead, the enzymes should be sprinkled on soft, non-acidic foods or swallowed whole with a glass of water or juice.

A. Pancreatic enzymes are generally safe and well-tolerated when taken as prescribed but they can cause side effects in some individuals. Common side effects may include abdominal pain, diarrhea, constipation, nausea, and bloating.

B. Pancreatic enzymes help individuals with cystic fibrosis digest fat, as well as proteins and carbohydrates. In cystic fibrosis, the pancreas does not produce enough digestive enzymes, leading to malabsorption of nutrients, particularly fat. Supplemental pancreatic enzymes help compensate for this deficiency and improve nutrient absorption.

C. Pancreatic enzymes are typically taken with meals or snacks to aid in digestion. However, if the child is consuming a small meal or snack that contains minimal fat, the enzymes may not be necessary. It's important for the mother to follow the healthcare provider's instructions regarding when and how to administer the enzymes.