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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).
The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?

"CF is inherited through an X-linked dominant pattern.”

"CF is an autosomal recessive genetic disorder.”

"CF is inherited when a child inherits a defective CFTR gene from one parent.”

"CF is solely caused by the deletion of phenylalanine at position 508 (F508del).”

Answer and Explanation

The Correct Answer is B

"CF is an autosomal recessive genetic disorder.”.

Choice A rationale:

CF is not inherited through an X-linked dominant pattern.

X-linked inheritance involves genes located on the X chromosome, and CF is not linked to this type of inheritance.

Choice C rationale:

CF is not solely related to inheriting a defective CFTR gene from one parent.

While inheriting a mutated CFTR gene is a factor, CF is an autosomal recessive disorder, meaning it requires mutations in both copies of the CFTR gene (one from each parent) for the disease to manifest.

Choice D rationale:

CF is not solely caused by the deletion of phenylalanine at position 508 (F508del).

While this mutation is one of the most common causes of CF, it is not the only genetic variation associated with the disease.

CF can result from various mutations in the CFTR gene.

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Correct Answer is B

Explanation

Choice A rationale:

Avoiding high-calorie foods to prevent weight gain is not an appropriate nursing intervention for a child with cystic fibrosis.

These children often have difficulty maintaining their weight due to malabsorption, and they may need a high-calorie diet to ensure proper growth and development.

Choice C rationale:

Disregarding the diet's impact on cystic fibrosis is not a valid approach.

Nutrition plays a crucial role in managing the condition, and dietary choices can significantly impact a child's health and well-being.

The statement is inaccurate and should not be followed.

Choice D rationale:

Limiting food intake to avoid digestive issues is not a suitable approach for a child with cystic fibrosis.

While digestive issues can be a concern, it is essential to provide adequate nutrition to support growth and development.

Restricting food intake can lead to malnutrition in these patients.

A. Administer respiratory treatments, including chest physiotherapy. B. Encourage a low-calorie, low-protein diet. C. Emphasize the importance of hand hygiene. D. Provide psychological counseling and support. E. Avoid exercise and physical activity.

Correct Answer is ["A","C","D"]

Explanation

Administer respiratory treatments, including chest physiotherapy.

C. Emphasize the importance of hand hygiene.

D. Provide psychological counseling and support.

Choice A rationale:

Administering respiratory treatments, including chest physiotherapy, is essential in managing cystic fibrosis in children.

Cystic fibrosis often results in thick, sticky mucus in the lungs, making it difficult to clear airway secretions.

Chest physiotherapy helps loosen and mobilize these secretions, improving lung function and reducing the risk of respiratory infections.

Choice B rationale:

Encouraging a low-calorie, low-protein diet is not an appropriate intervention for managing cystic fibrosis in children.

Children with cystic fibrosis typically have increased nutritional needs due to malabsorption of nutrients, and a low-calorie, low-protein diet could exacerbate their nutritional deficiencies and growth issues.

Choice C rationale:

Emphasizing the importance of hand hygiene is a crucial nursing intervention for managing cystic fibrosis in children.

Cystic fibrosis patients are more susceptible to respiratory infections, and good hand hygiene helps prevent the spread of infections, which is especially important in a healthcare setting.

Choice D rationale:

Providing psychological counseling and support is essential for children with cystic fibrosis.

The chronic nature of the disease, frequent hospitalizations, and daily treatments can take a toll on a child's mental health.

Psychological support helps them cope with the emotional challenges and stress associated with their condition.

Choice E rationale:

Avoiding exercise and physical activity is not an appropriate intervention for managing cystic fibrosis in children.

Physical activity is beneficial for maintaining lung function and overall health in individuals with cystic fibrosis.

It helps improve airway clearance and strengthen respiratory muscles.

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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?

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Naxlex Comprehensive Predictor Exams

A nurse is caring for a child with cystic fibrosis.The nurse is responsible for providing nutritional support as part of the treatment plan.What is an appropriate nursing intervention in this context?

Correct Answer is B

Explanation

Select all the nursing interventions appropriate for managing cystic fibrosis in children:.

Correct Answer is ["A","C","D"]

Explanation

A nurse is teaching a group of parents about managing cystic fibrosis (CF) in children.Which of the following interventions should the nurse include in the teaching? (Select all that apply).

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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?

A nurse is providing psychosocial support to a child with cystic fibrosis.What is an essential aspect of this support?

A nurse is assessing a child with cystic fibrosis.The child presents with chronic cough, wheezing, and recurrent respiratory infections.What should the nurse expect to find during this assessment?

A nurse is caring for a child with cystic fibrosis (CF) and is assessing the child's respiratory status.Which of the following findings should the nurse consider as a common respiratory complication of CF?

A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).
The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?