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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).
The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?

"CF is inherited through an X-linked dominant pattern.”

"CF is an autosomal recessive genetic disorder.”

"CF is inherited when a child inherits a defective CFTR gene from one parent.”

"CF is solely caused by the deletion of phenylalanine at position 508 (F508del).”

Answer and Explanation

The Correct Answer is B

"CF is an autosomal recessive genetic disorder.”.

Choice A rationale:

CF is not inherited through an X-linked dominant pattern.

X-linked inheritance involves genes located on the X chromosome, and CF is not linked to this type of inheritance.

Choice C rationale:

CF is not solely related to inheriting a defective CFTR gene from one parent.

While inheriting a mutated CFTR gene is a factor, CF is an autosomal recessive disorder, meaning it requires mutations in both copies of the CFTR gene (one from each parent) for the disease to manifest.

Choice D rationale:

CF is not solely caused by the deletion of phenylalanine at position 508 (F508del).

While this mutation is one of the most common causes of CF, it is not the only genetic variation associated with the disease.

CF can result from various mutations in the CFTR gene.

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Correct Answer is A

Explanation

"You'll need to take bronchodilators as prescribed.”.

Choice A rationale:

Bronchodilators are commonly prescribed to children with cystic fibrosis to help open airways, making it easier for them to breathe.

These medications assist in relieving airway constriction and improving respiratory function.

Choice B rationale:

Stating that "antibiotics are unnecessary for cystic fibrosis" is incorrect.

Antibiotics are often required for cystic fibrosis patients to treat and prevent respiratory infections, which are common due to the thick mucus buildup in the airways.

Choice C rationale:

Mucolytics are medications that help thin and mobilize mucus in the airways.

Advising the child to "avoid mucolytics" is not appropriate, as these drugs can be beneficial in managing cystic fibrosis by facilitating mucus clearance and reducing the risk of lung infections.

Choice D rationale:

Telling the child to "skip the medications; they won't help" is incorrect and potentially dangerous advice.

Medications prescribed for cystic fibrosis are essential for managing the disease, and skipping them can lead to worsened symptoms and complications.

A. Encourage physical activity and exercise. B. Administer pancreatic enzyme replacement therapy. C. Restrict fluid intake to reduce mucus production. D. Teach airway clearance techniques. E. Promote a high-fat, high-calorie diet.

Correct Answer is ["A","B","D","E"]

Explanation

Choice A rationale:

Encouraging physical activity and exercise is important in managing CF.

It helps improve lung function and overall health in individuals with CF.

Choice B rationale:

Administering pancreatic enzyme replacement therapy is a crucial part of CF management.

CF often affects the pancreas, leading to malabsorption, and these enzymes help digest and absorb nutrients properly.

Choice C rationale:

Restricting fluid intake to reduce mucus production is not a recommended intervention for CF.

Hydration is essential to keep mucus from becoming too thick and sticky.

Dehydration can worsen mucus obstruction.

Choice D rationale:

Teaching airway clearance techniques is essential in CF management.

It helps individuals clear the thick mucus from their airways, promoting better lung function.

Choice E rationale:

Promoting a high-fat, high-calorie diet is important for individuals with CF.

CF often leads to malnutrition, and a high-calorie diet helps maintain proper nutrition and growth.

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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?

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Naxlex Comprehensive Predictor Exams

A nurse is discussing treatment options with a child who has cystic fibrosis.What pharmacological interventions might be part of the treatment plan for this child?

Correct Answer is A

Explanation

A nurse is teaching a group of parents about managing cystic fibrosis (CF) in children.Which of the following interventions should the nurse include in the teaching? (Select all that apply).

Correct Answer is ["A","B","D","E"]

Explanation

Select all the nursing interventions appropriate for managing cystic fibrosis in children:.

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A nurse is providing education to a parent of a child newly diagnosed with cystic fibrosis (CF).
The parent asks, "How is CF inherited?" Which of the following statements by the nurse is correct?