Which type of immunodeficiency disorder is inherited in an X-linked recessive pattern and primarily affects males, leading to the absence of mature B cells and immunoglobulins?
Selective IgA deficiency
DiGeorge syndrome
X-linked agammaglobulinemia
Severe combined immunodeficiency (SCID)
The Correct Answer is C
Explanation: The correct answer is c. X-linked agammaglobulinemia. This disorder primarily affects males and is caused by mutations in the BTK gene, resulting in a lack of mature B cells and immunoglobulins.
Incorrect choices:
a. Selective IgA deficiency is a primary immunodeficiency disorder characterized by a deficiency of immunoglobulin A (IgA), and it can affect both males and females.
b. DiGeorge syndrome is caused by a chromosome 22 deletion and is not inherited in an X-linked recessive pattern.
d. Severe combined immunodeficiency (SCID) is a group of disorders that can be inherited in various patterns, including autosomal recessive, autosomal dominant, or X-linked recessive. SCID affects both males and females and results in a severe deficiency of T cells, B cells, and natural killer (NK) cells.
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Related Questions
Correct Answer is C
Explanation
Explanation: The correct answer is c. Administer intramuscular immunoglobulins (IG) as ordered. For clients with immunodeficiency disorders, intramuscular immunoglobulins can be prescribed to provide passive immunity and help prevent infections. Immunoglobulins contain antibodies that the client's immune system may be lacking, offering protection against various pathogens.
Incorrect choices:
a. Encouraging the client to receive live vaccines is not appropriate for clients with immunodeficiency disorders. Live vaccines contain live, attenuated viruses or bacteria, which can cause severe infections in individuals with compromised immune systems.
b. Prescribing broad-spectrum antibiotics prophylactically may be used in some cases, but it is not the first-line treatment for immunodeficiency disorders. It is essential to identify the specific pathogens causing infections before initiating antibiotic therapy to avoid antimicrobial resistance.
d. Initiating high-dose corticosteroid therapy is not appropriate for the management of immunodeficiency disorders. Corticosteroids can suppress the immune system further and increase the risk of infections in these clients.
Correct Answer is C
Explanation
Explanation: The correct answer is c. Limit visitors to family members only. Clients with immunodeficiency disorders are at increased risk of infections, and limiting visitors to family members only can help reduce the risk of exposure to infectious agents. It is essential to create a controlled and safe environment for these clients.
Incorrect choices:
a. Encouraging the client to interact with other clients in the unit can increase the risk of exposure to infections and is not appropriate for someone with immunodeficiency.
b. Live vaccines contain weakened pathogens and are contraindicated for clients with immunodeficiency disorders, as they can cause serious infections in this population.
d. Providing the client with a private room with negative pressure is not necessary for every client with immunodeficiency disorder. Negative pressure rooms are used for clients with specific airborne infectious diseases, and the decision to use such rooms is based on the specific circumstances of each client.
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